A rare variant of neuroenteric cyst: split notochord syndrome
نویسندگان
چکیده
منابع مشابه
[A rare variant of neuroenteric cyst: split notochord syndrome].
OBJECTIVE We present a case of split notochord syndrome, an extremely rare form of spinal dysraphism. DESCRIPTION We treated a 2 month-old boy presenting with an extensive lumbosacral deformity, hydrocephalus and apparent enteric segments in the dorsal midline, accompanied by an enteric fistula and imperforated anus. The malformation was diagnosed as split notochord syndrome. The baby died as...
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We treated a one day old baby presenting with an extensive lumbosacral deformity, hydrocephalus and apparent enteric segments in the dorsal midline with abnormal genitalia, accompanied by an enteric fistula and imperforated anus. The malformation fits into split notochord syndrome. The baby died as a result of sepsis before surgical treatment could be attempted. Patient was full term caesarian ...
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ژورنال
عنوان ژورنال: Jornal de Pediatria
سال: 2004
ISSN: 0021-7557
DOI: 10.2223/1138